netFormulary NHS
Shropshire and Telford Local Health Economy
Shropshire, Telford and Wrekin CCG
Shrewsbury and Telford Hospitals NHS Trust
Robert Jones & Agnes Hunt Orthopaedic Hospital NHS Foundation Trust
Shropshire Community Health NHS Trust
 Formulary Chapter 9: Nutrition and blood - Full Chapter
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09.08.01  Expand sub section  Drugs used in metabolic disorders
09.08.01  Expand sub section  Wilsons disease
09.08.01  Expand sub section  Carnitine deficiency
09.08.01  Expand sub section  Fabry's disease
09.08.01  Expand sub section  Gaucher's disease to top
09.08.01  Expand sub section  Pompe disease
Alglucosidase Alfa (Myozyme)
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Restricted Drug Restricted
High Cost Medicine
NHS England


This drug is NHSE funded for the indication outlined within the Ex-Tariff list.

09.08.01  Expand sub section  Urea cycle disorders
note Notes
Section Title Section Title (top level)
Section Title Section Title (sub level)
First Choice Item First Choice item
Non Formulary Item Non Formulary section
Restricted Drug
Restricted Drug
Unlicensed Drug
Track Changes
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Link to adult BNF
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Link to children's BNF
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Link to SPCs
Cytotoxic Drug
Cytotoxic Drug
Controlled Drug
High Cost Medicine
High Cost Medicine
Cancer Drugs Fund
Cancer Drugs Fund
NHS England

Traffic Light Status Information

Status Description


Suitable first-line drugs for implementation in Primary Care  


These medicines are considered suitable for prescribing in Primary Care following specialist (consultant or GPwSI) initiation or recommendation. Some of these medicines may require on-going communication between the Secondary Care specialist and the Primary Care prescriber using Prescribing Information (PI) or through the use of an Effective Shared Care Agreement (ESCA) and this will be indicated in the text.  


Drugs which require special consideration. These are drugs for use in Secondary Care ONLY, Consultant Prescribing ONLY or by Tertiary Centres ONLY where indicated in the text. They should not be prescribed in Primary Care.  


Medicines classified in the BNF as 'not NHS' or are considered by the Area Prescribing Committee to be of low clinical value should not be prescribed